Persistent hyperplastic primary vitreous (PHPV)
This is a rare unilateral condition. Most cases seen in the
examination will be of the less severe form. Less commonly
you may have a patient with leukocoria and microphthalmos.
The picture seen here is of the posterior type of PHPV. The
optic disc contains dense, white fibrous tissue extending towards
the ora serrata (usually inferiorly). The retinal vessels are distorted
as they emerge from the optic disc.
- posterior PHPV may resemble retinopathy of prematurity
with dragged disc. In retinopathy of prematurity, a ridge
is usually seen in the periphery
- the patient may have microphthalmos ± esotropia
1. Which conditions may simulate PHPV?Answer
2. What are the complications of PHPV?