Right sided port-wine stain of the face and ipsilateral
Left-sided port-wine stain with conjunctival
involvement. The patient also has left glaucoma.
The face of this patient has a port-wine in the distribution of the first and second divison of the trigeminal nerve.
The ipsilateral eye may be red (due to the presence of haemangioma of the conjunctiva; the iris may be involved
causing heterochromic iridis). The affected side of the face may also show hypertrophy.
- examine the anterior segment for haemangioma and the presence of trabeculectomy
- posterior segment for glaucomatous disc and choroidal haemangioma (this is diffuse and may cause exudative
1. What is the inheritance of Sturge-Weber's syndrome?
2. What is responsible for the port-wine stain and can it be removed?