This female patient who has retinal lesion has these skin 
   lesions since birth

   a. What is the likely diagnosis?

   b. How is this condition inherited?

   c. List the ocular features that may occur.

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Answers:
 
 This female patient who has retinal lesion has these skin lesions since birth.

 a. What is the likely diagnosis?

Incontinential pigmenti (Bloch-Sulzberger syndrome).

In this inherited condition, the patient develops linear skin eruption at infancy.These eruptions later resolved leaving behind linear pigmentation.Non-ocular features include: abnormal denture and nails, mental retardation (30% of cases) and alopecia.

b. How is this condition inherited?
X-linked dominant. The condition is lethal to male.
 c. List the ocular features that may occur.
    • Strabismus
    • Nystagmus
    • Peripheral fibrovascular proliferation of the retina.
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